C83.390

Primary central nervous system lymphoma

Billable / specificHCC V28 20

C83.390 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • PCNSL of brain
  • PCNSL of meninges
  • PCNSL of spinal cord
  • PCNSL NOS

Includes (from C83)

  • Note: Functional activity
  • Note: All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Note: Morphology [Histology]
  • Note: Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Note: Primary malignant neoplasms overlapping site boundaries
  • Note: A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Note: Malignant neoplasm of ectopic tissue
  • Note: Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

Excludes1

Not coded here — never report together with this code.

  • Primary central nervous system lymphoma, Burkitt (C83.79)
  • Primary central nervous system lymphoma, lymphoblastic (C83.59)
  • Primary central nervous system lymphoma, other (C83.89)
  • Primary central nervous system lymphoma, peripheral T-cell (C84.49)
  • mediastinal (thymic) large B-cell lymphoma (C85.2-) (from C83.3)
  • mature T/NK-cell lymphomas (C84.-) (from C83.3)
  • personal history of non-Hodgkin lymphoma (Z85.72) (from C83)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Kaposi's sarcoma of lymph nodes (C46.3) (from C83)
  • secondary and unspecified neoplasm of lymph nodes (C77.-) (from C83)
  • secondary neoplasm of bone marrow (C79.52) (from C83)
  • secondary neoplasm of spleen (C78.89) (from C83)

Also known as

  • PCNSL of brain
  • PCNSL of meninges
  • PCNSL of spinal cord
  • PCNSL NOS
  • Lymphoma, diffuse large cell, primary central nervous system
  • Lymphoma, primary central nervous system
  • Lymphoma, primary central nervous system, diffuse large B-cell

Parent code

  • C83.39Diffuse large B-cell lymphoma, extranodal and solid organ sitesHeader

Related codes

  • C83.398Diffuse large B-cell lymphoma of other extranodal and solid organ sitesBillable

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