C88.0

Waldenstrom macroglobulinemia

Non-billable header

C88.0 is a non-billable header code. Use one of the more specific codes below.

Inclusion terms

Applicable to

  • Lymphoplasmacytic lymphoma with IgM-production
  • Macroglobulinemia (idiopathic) (primary)

Includes (from C88)

  • Note: Functional activity
  • Note: All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Note: Morphology [Histology]
  • Note: Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Note: Primary malignant neoplasms overlapping site boundaries
  • Note: A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Note: Malignant neoplasm of ectopic tissue
  • Note: Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

Excludes1

Not coded here — never report together with this code.

  • small cell B-cell lymphoma (C83.0)
  • B-cell lymphoma, unspecified (C85.1-) (from C88)
  • personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79) (from C88)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Kaposi's sarcoma of lymph nodes (C46.3) (from C88)
  • secondary and unspecified neoplasm of lymph nodes (C77.-) (from C88)
  • secondary neoplasm of bone marrow (C79.52) (from C88)
  • secondary neoplasm of spleen (C78.89) (from C88)

Also known as

  • Lymphoplasmacytic lymphoma with IgM-production
  • Macroglobulinemia (idiopathic) (primary)
  • Disorder, glomerular, Waldenström macroglobulinemia
  • Glomerulonephritis, in Waldenström macroglobulinemia
  • Lymphoma, lymphoplasmacytic, with IgM-production
  • Macroglobulinemia
  • Macroglobulinemia, Waldenström
  • Waldenström, syndrome or macroglobulinemia

Parent code

  • C88Malignant immunoproliferative diseases and certain other B-cell lymphomasHeader

More specific codes C88.0

  • C88.00Waldenstrom macroglobulinemia not having achieved remissionBillable
  • C88.01Waldenstrom macroglobulinemia, in remissionBillable

Related codes

  • C88.2Heavy chain diseaseHeader
  • C88.3Immunoproliferative small intestinal diseaseHeader
  • C88.4Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]Header
  • C88.8Other malignant immunoproliferative diseasesHeader
  • C88.9Malignant immunoproliferative disease, unspecifiedHeader

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