C88.30

Immunoproliferative small intestinal disease not having achieved remission

Billable / specificHCC V28 21

C88.30 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Alpha heavy chain disease NOS
  • Alpha heavy chain disease not having achieved remission
  • Alpha heavy chain disease with failed remission
  • Immunoproliferative small intestinal disease NOS
  • Immunoproliferative small intestinal disease with failed remission
  • Mediterranean lymphoma NOS
  • Mediterranean lymphoma not having achieved remission
  • Mediterranean lymphoma with failed remission

Includes (from C88)

  • Note: Functional activity
  • Note: All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Note: Morphology [Histology]
  • Note: Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Note: Primary malignant neoplasms overlapping site boundaries
  • Note: A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Note: Malignant neoplasm of ectopic tissue
  • Note: Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

Excludes1

Not coded here — never report together with this code.

  • B-cell lymphoma, unspecified (C85.1-) (from C88)
  • personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79) (from C88)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Kaposi's sarcoma of lymph nodes (C46.3) (from C88)
  • secondary and unspecified neoplasm of lymph nodes (C77.-) (from C88)
  • secondary neoplasm of bone marrow (C79.52) (from C88)
  • secondary neoplasm of spleen (C78.89) (from C88)

Also known as

  • Alpha heavy chain disease NOS
  • Alpha heavy chain disease not having achieved remission
  • Alpha heavy chain disease with failed remission
  • Immunoproliferative small intestinal disease NOS
  • Immunoproliferative small intestinal disease with failed remission
  • Mediterranean lymphoma NOS
  • Mediterranean lymphoma not having achieved remission
  • Mediterranean lymphoma with failed remission

Parent code

  • C88.3Immunoproliferative small intestinal diseaseHeader

Related codes

  • C88.31Immunoproliferative small intestinal disease, in remissionBillable

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