D51.0

Vitamin B12 deficiency anemia due to intrinsic factor deficiency

Billable / specific

D51.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Addison anemia
  • Biermer anemia
  • Pernicious (congenital) anemia
  • Congenital intrinsic factor deficiency

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9) (from D51)
  • certain conditions originating in the perinatal period (P00-P96) (from D51)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D51)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D51)
  • endocrine, nutritional and metabolic diseases (E00-E88) (from D51)
  • human immunodeficiency virus [HIV] disease (B20) (from D51)
  • injury, poisoning and certain other consequences of external causes (S00-T88) (from D51)
  • neoplasms (C00-D49) (from D51)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D51)
  • deficiency of other B group vitamins (E53-) (from D51)

Also known as

  • Addison anemia
  • Biermer anemia
  • Pernicious (congenital) anemia
  • Congenital intrinsic factor deficiency
  • Addison's, anemia
  • Addison-Biermer anemia
  • Anemia, Addison
  • Anemia, Biermer's
  • Anemia, combined system disease NEC
  • Anemia, congenital, pernicious
  • Anemia, cytogenic
  • Anemia, deficiency, vitamin B12 NOS, pernicious
  • Anemia, malignant
  • Anemia, pernicious
  • Anemia, progressive, malignant
  • Anemia, progressive, pernicious
  • Anemia, vitamin, B12 deficiencypernicious
  • Biermer'sanemia or disease
  • Congenital, intrinsic factor deficiency

Parent code

  • D51Vitamin B12 deficiency anemiaHeader

Related codes

  • D51.1Vitamin B12 deficiency anemia due to selective vitamin B12 malabsorption with proteinuriaBillable
  • D51.2Transcobalamin II deficiencyBillable
  • D51.3Other dietary vitamin B12 deficiency anemiaBillable
  • D51.8Other vitamin B12 deficiency anemiasBillable
  • D51.9Vitamin B12 deficiency anemia, unspecifiedBillable

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