D59.5

Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]

Billable / specificHCC V28 109

D59.5 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Excludes1

Not coded here — never report together with this code.

  • hemoglobinuria NOS (R82.3)

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9) (from D59)
  • certain conditions originating in the perinatal period (P00-P96) (from D59)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D59)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D59)
  • endocrine, nutritional and metabolic diseases (E00-E88) (from D59)
  • human immunodeficiency virus [HIV] disease (B20) (from D59)
  • injury, poisoning and certain other consequences of external causes (S00-T88) (from D59)
  • neoplasms (C00-D49) (from D59)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D59)

Also known as

  • Hematuria, paroxysmal, nocturnal
  • Hemoglobinemia, paroxysmal, nocturnal
  • Hemoglobinuria, nocturnal
  • Hemoglobinuria, paroxysmal, nocturnal
  • Marchiafava-Micheli syndrome

Parent code

  • D59Acquired hemolytic anemiaHeader

Related codes

  • D59.0Drug-induced autoimmune hemolytic anemiaBillable
  • D59.1Other autoimmune hemolytic anemiasHeader
  • D59.2Drug-induced nonautoimmune hemolytic anemiaBillable
  • D59.3Hemolytic-uremic syndromeHeader
  • D59.4Other nonautoimmune hemolytic anemiasBillable
  • D59.6Hemoglobinuria due to hemolysis from other external causesBillable
  • D59.8Other acquired hemolytic anemiasBillable
  • D59.9Acquired hemolytic anemia, unspecifiedBillable

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