Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
Billable / specificHCC V28 109
D59.5 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Excludes1
Not coded here — never report together with this code.
- hemoglobinuria NOS (R82.3)
Excludes2
Not included here — may be reported together when both conditions exist.
- autoimmune disease (systemic) NOS (M35.9) (from D59)
- certain conditions originating in the perinatal period (P00-P96) (from D59)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D59)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D59)
- endocrine, nutritional and metabolic diseases (E00-E88) (from D59)
- human immunodeficiency virus [HIV] disease (B20) (from D59)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from D59)
- neoplasms (C00-D49) (from D59)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D59)
Also known as
- Hematuria, paroxysmal, nocturnal
- Hemoglobinemia, paroxysmal, nocturnal
- Hemoglobinuria, nocturnal
- Hemoglobinuria, paroxysmal, nocturnal
- Marchiafava-Micheli syndrome
Parent code
- D59Acquired hemolytic anemiaHeader
Related codes
- D59.0Drug-induced autoimmune hemolytic anemiaBillable
- D59.1Other autoimmune hemolytic anemiasHeader
- D59.2Drug-induced nonautoimmune hemolytic anemiaBillable
- D59.3Hemolytic-uremic syndromeHeader
- D59.4Other nonautoimmune hemolytic anemiasBillable
- D59.6Hemoglobinuria due to hemolysis from other external causesBillable
- D59.8Other acquired hemolytic anemiasBillable
- D59.9Acquired hemolytic anemia, unspecifiedBillable