D61.09

Other constitutional aplastic anemia

Billable / specificHCC V28 109

D61.09 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Pancytopenia with malformations

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9) (from D61)
  • certain conditions originating in the perinatal period (P00-P96) (from D61)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D61)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D61)
  • endocrine, nutritional and metabolic diseases (E00-E88) (from D61)
  • human immunodeficiency virus [HIV] disease (B20) (from D61)
  • injury, poisoning and certain other consequences of external causes (S00-T88) (from D61)
  • neoplasms (C00-D49) (from D61)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D61)
  • neutropenia (D70.-) (from D61)

Also known as

  • Pancytopenia with malformations
  • Aleukia, hemorrhagica, congenital
  • Anemia, aplastic, congenital
  • Anemia, aregenerative, congenital
  • Anemia, chronica congenita aregenerativa
  • Anemia, congenital, aplastic
  • Erythroblastophthisis
  • Erythrogenesis imperfecta
  • Pancytopenia, with malformations
  • Pancytopenia, congenital
  • Panhematopenia, congenital
  • Panhematopenia, constitutional
  • Panhemocytopenia, congenital
  • Panhemocytopenia, constitutional
  • Panmyelopathy, familial, constitutional
  • Panmyelophthisis, congenital

Parent code

  • D61.0Constitutional aplastic anemiaHeader

Related codes

  • D61.01Constitutional (pure) red blood cell aplasiaBillable
  • D61.02Shwachman-Diamond syndromeBillable
  • D61.03Fanconi anemiaBillable

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