Congenital agranulocytosis
Billable / specificHCC V28 115
D70.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Congenital neutropenia
- Infantile genetic agranulocytosis
- Kostmann's disease
Includes (from D70)
- agranulocytosis
- decreased absolute neurophile count (ANC)
Excludes1
Not coded here — never report together with this code.
Excludes2
Not included here — may be reported together when both conditions exist.
- autoimmune disease (systemic) NOS (M35.9) (from D70)
- certain conditions originating in the perinatal period (P00-P96) (from D70)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D70)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D70)
- endocrine, nutritional and metabolic diseases (E00-E88) (from D70)
- human immunodeficiency virus [HIV] disease (B20) (from D70)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from D70)
- neoplasms (C00-D49) (from D70)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D70)
Use additional code
Add a code to identify the following, if applicable.
Code also
An additional code may be needed.
Also known as
- Congenital neutropenia
- Infantile genetic agranulocytosis
- Kostmann's disease
- Agranulocytosis, congenital
- Aleukia, congenital
- Disease, diseased, Kostmann's
- Leukopenia, congenital
- Leukopenia, cyclic
- Leukopenia, familial
- Leukopenia, infantile genetic
- Leukopenia, periodic
- Neutropenia, neutropenic, congenital
- Syndrome, Kostmann's
Parent code
- D70NeutropeniaHeader