Congenital methemoglobinemia
Billable / specific
D74.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Congenital NADH-methemoglobin reductase deficiency
- Hemoglobin-M [Hb-M] disease
- Methemoglobinemia, hereditary
Excludes2
Not included here — may be reported together when both conditions exist.
- autoimmune disease (systemic) NOS (M35.9) (from D74)
- certain conditions originating in the perinatal period (P00-P96) (from D74)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D74)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D74)
- endocrine, nutritional and metabolic diseases (E00-E88) (from D74)
- human immunodeficiency virus [HIV] disease (B20) (from D74)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from D74)
- neoplasms (C00-D49) (from D74)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D74)
Also known as
- Congenital NADH-methemoglobin reductase deficiency
- Hemoglobin-M [Hb-M] disease
- Methemoglobinemia, hereditary
- Deficiency, deficient, NADH diaphorase or reductase
- Deficiency, deficient, NADH-methemoglobin reductase
- Disease, diseased, diaphorase deficiency
- Disease, diseased, hemoglobin or Hb, M
- Methemoglobinemia, congenital
- Methemoglobinemia, enzymatic
- Methemoglobinemia, Hb M disease
Parent code
- D74MethemoglobinemiaHeader