E71.11

Branched-chain organic acidurias

Non-billable header

E71.11 is a non-billable header code. Use one of the more specific codes below.

Inclusion terms

Includes (from E71)

  • Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Excludes1

Not coded here — never report together with this code.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E71)
  • androgen insensitivity syndrome (E34.5-) (from E71)
  • congenital adrenal hyperplasia (E25.0) (from E71)
  • hemolytic anemias attributable to enzyme disorders (D55.-) (from E71)
  • Marfan syndrome (Q87.4-) (from E71)
  • 5-alpha-reductase deficiency (E29.1) (from E71)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Ehlers-Danlos syndromes (Q79.6-) (from E71)

Parent code

  • E71.1Other disorders of branched-chain amino-acid metabolismHeader

More specific codes E71.11

  • E71.110Isovaleric acidemiaBillable
  • E71.1113-methylglutaconic aciduriaBillable
  • E71.118Other branched-chain organic aciduriasBillable

Related codes

  • E71.12Disorders of propionate metabolismHeader
  • E71.19Other disorders of branched-chain amino-acid metabolismBillable

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