E71.31

Disorders of fatty-acid oxidation

Non-billable header

E71.31 is a non-billable header code. Use one of the more specific codes below.

Inclusion terms

Includes (from E71)

  • Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Excludes1

Not coded here — never report together with this code.

  • peroxisomal disorders (E71.5) (from E71.3)
  • Refsum's disease (G60.1) (from E71.3)
  • Schilder's disease (G37.0) (from E71.3)
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E71)
  • androgen insensitivity syndrome (E34.5-) (from E71)
  • congenital adrenal hyperplasia (E25.0) (from E71)
  • hemolytic anemias attributable to enzyme disorders (D55.-) (from E71)
  • Marfan syndrome (Q87.4-) (from E71)
  • 5-alpha-reductase deficiency (E29.1) (from E71)

Excludes2

Not included here — may be reported together when both conditions exist.

  • carnitine deficiency due to inborn error of metabolism (E71.42) (from E71.3)
  • Ehlers-Danlos syndromes (Q79.6-) (from E71)

Parent code

  • E71.3Disorders of fatty-acid metabolismHeader

More specific codes E71.31

  • E71.310Long chain/very long chain acyl CoA dehydrogenase deficiencyBillable
  • E71.311Medium chain acyl CoA dehydrogenase deficiencyBillable
  • E71.312Short chain acyl CoA dehydrogenase deficiencyBillable
  • E71.313Glutaric aciduria type IIBillable
  • E71.314Muscle carnitine palmitoyltransferase deficiencyBillable
  • E71.318Other disorders of fatty-acid oxidationBillable

Related codes

  • E71.30Disorder of fatty-acid metabolism, unspecifiedBillable
  • E71.32Disorders of ketone metabolismBillable
  • E71.39Other disorders of fatty-acid metabolismBillable

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