Defects in glycoprotein degradation
Billable / specific
E77.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Aspartylglucosaminuria
- Fucosidosis
- Mannosidosis
- Sialidosis [mucolipidosis I]
Includes (from E77)
- Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Excludes1
Not coded here — never report together with this code.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E77)
- androgen insensitivity syndrome (E34.5-) (from E77)
- congenital adrenal hyperplasia (E25.0) (from E77)
- hemolytic anemias attributable to enzyme disorders (D55.-) (from E77)
- Marfan syndrome (Q87.4-) (from E77)
- 5-alpha-reductase deficiency (E29.1) (from E77)
Excludes2
Not included here — may be reported together when both conditions exist.
Also known as
- Aspartylglucosaminuria
- Fucosidosis
- Mannosidosis
- Sialidosis [mucolipidosis I]
- Defect, defective, degradation, glycoprotein
- Defect, defective, glycoprotein degradation
- Mucolipidosis, I
- Sialidosis
Parent code
- E77Disorders of glycoprotein metabolismHeader