E78.3

Hyperchylomicronemia

Billable / specific

E78.3 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Chylomicron retention disease
  • Fredrickson's hyperlipoproteinemia, type I or V
  • Hyperlipidemia, group D
  • Mixed hyperglyceridemia

Includes (from E78)

  • Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Excludes1

Not coded here — never report together with this code.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E78)
  • androgen insensitivity syndrome (E34.5-) (from E78)
  • congenital adrenal hyperplasia (E25.0) (from E78)
  • hemolytic anemias attributable to enzyme disorders (D55.-) (from E78)
  • Marfan syndrome (Q87.4-) (from E78)
  • 5-alpha-reductase deficiency (E29.1) (from E78)
  • sphingolipidosis (E75.0-E75.3) (from E78)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Ehlers-Danlos syndromes (Q79.6-) (from E78)

Also known as

  • Chylomicron retention disease
  • Fredrickson's hyperlipoproteinemia, type I or V
  • Hyperlipidemia, group D
  • Mixed hyperglyceridemia
  • Bürger-Grütz disease or syndrome
  • Chylomicronemia
  • Disease, diseased, Bürger-Grütz
  • Disease, diseased, chylomicron retention
  • Frederickson's hyperlipoproteinemia, type, I and V
  • Hepatosplenomegaly, hyperlipemic
  • Hyperchylomicronemia, with hyperbetalipoproteinemia
  • Hyperglyceridemia, mixed
  • Hyperlipemia, hyperlipidemia, group, D
  • Hyperlipoproteinemia, Fredrickson's type, I
  • Hyperlipoproteinemia, Fredrickson's type, V
  • Lipemia, retina, retinalis
  • Lipidosis, hepatosplenomegalic
  • Prebetalipoproteinemia, with chylomicronemia

Parent code

  • E78Disorders of lipoprotein metabolism and other lipidemiasHeader

Related codes

  • E78.0Pure hypercholesterolemiaHeader
  • E78.1Pure hyperglyceridemiaBillable
  • E78.2Mixed hyperlipidemiaBillable
  • E78.4Other hyperlipidemiaHeader
  • E78.5Hyperlipidemia, unspecifiedBillable
  • E78.6Lipoprotein deficiencyBillable
  • E78.7Disorders of bile acid and cholesterol metabolismHeader
  • E78.8Other disorders of lipoprotein metabolismHeader
  • E78.9Disorder of lipoprotein metabolism, unspecifiedBillable

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