Acute intermittent (hepatic) porphyria
Billable / specificHCC V28 50
E80.21 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Includes (from E80)
- defects of catalase and peroxidase
- Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Excludes1
Not coded here — never report together with this code.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E80)
- androgen insensitivity syndrome (E34.5-) (from E80)
- congenital adrenal hyperplasia (E25.0) (from E80)
- hemolytic anemias attributable to enzyme disorders (D55.-) (from E80)
- Marfan syndrome (Q87.4-) (from E80)
- 5-alpha-reductase deficiency (E29.1) (from E80)
Excludes2
Not included here — may be reported together when both conditions exist.
Also known as
- Porphyria, acute intermittent
Parent code
- E80.2Other and unspecified porphyriaHeader