E83.821

ENPP1 deficiency causing generalized arterial calcification of infancy

Billable / specific

E83.821 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from E83)

  • Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Excludes1

Not coded here — never report together with this code.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E83)
  • androgen insensitivity syndrome (E34.5-) (from E83)
  • congenital adrenal hyperplasia (E25.0) (from E83)
  • hemolytic anemias attributable to enzyme disorders (D55.-) (from E83)
  • Marfan syndrome (Q87.4-) (from E83)
  • 5-alpha-reductase deficiency (E29.1) (from E83)
  • dietary mineral deficiency (E58-E61) (from E83)
  • parathyroid disorders (E20-E21) (from E83)
  • vitamin D deficiency (E55.-) (from E83)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Ehlers-Danlos syndromes (Q79.6-) (from E83)

Code also

An additional code may be needed.

  • , if applicable, associated conditions such as:
  • heart failure (I50.-)
  • other secondary hypertension (I15.8)

Also known as

  • Deficiency, deficient, ENPP1, causing generalized arterial calcification of infancy

Parent code

  • E83.82Disorders of pyrophosphate metabolismHeader

Related codes

  • E83.820Generalized arterial calcification of infancy with unspecified genetic causalityBillable
  • E83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2Billable
  • E83.823ABCC6 deficiency causing generalized arterial calcification of infancyBillable
  • E83.824ABCC6 deficiency causing pseudoxanthoma elasticumBillable
  • E83.825CD73 deficiency causing arterial calcificationBillable

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