E84.0

Cystic fibrosis with pulmonary manifestations

Billable / specificHCC V28 277

E84.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from E84)

  • mucoviscidosis
  • Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Excludes1

Not coded here — never report together with this code.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E84)
  • androgen insensitivity syndrome (E34.5-) (from E84)
  • congenital adrenal hyperplasia (E25.0) (from E84)
  • hemolytic anemias attributable to enzyme disorders (D55.-) (from E84)
  • Marfan syndrome (Q87.4-) (from E84)
  • 5-alpha-reductase deficiency (E29.1) (from E84)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Ehlers-Danlos syndromes (Q79.6-) (from E84)

Use additional code

Add a code to identify the following, if applicable.

  • code to identify any infectious organism present, such as:
  • Pseudomonas (B96.5)

Code also

An additional code may be needed.

  • exocrine pancreatic insufficiency (K86.81) (from E84)

Also known as

  • Fibrosis, fibrotic, cystic, with pulmonary manifestations

Parent code

  • E84Cystic fibrosisHeader

Related codes

  • E84.1Cystic fibrosis with intestinal manifestationsHeader
  • E84.8Cystic fibrosis with other manifestationsBillable
  • E84.9Cystic fibrosis, unspecifiedBillable

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