F78.A9

Other genetic related intellectual disability

Billable / specific

F78.A9 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from F78)

  • disorders of psychological development

Excludes1

Not coded here — never report together with this code.

  • borderline intellectual functioning, IQ above 70 to 84 (R41.83) (from F78)

Excludes2

Not included here — may be reported together when both conditions exist.

  • symptoms, signs and abnormal clinical laboratory findings, not elsewhere classified (R00-R99) (from F78)

Code first

Sequence the underlying condition first.

  • any associated physical or developmental disorders (from F78)

Code also

An additional code may be needed.

  • , if applicable, any associated disorders

Also known as

  • Disability, disabilities, intellectual, with pathogenic CHAMP1
  • Disability, disabilities, intellectual, with pathogenic HNRNPH2
  • Disability, disabilities, intellectual, with pathogenic SATB2
  • Disability, disabilities, intellectual, with pathogenic SETBP1
  • Disability, disabilities, intellectual, with pathogenic STXBP1
  • Disability, disabilities, intellectual, autosomal dominant
  • Disability, disabilities, intellectual, autosomal recessive
  • Disability, disabilities, intellectual, genetic related
  • Disability, disabilities, intellectual, genetic related, specified NEC
  • Disability, disabilities, intellectual, in autosomal dominant mental retardation
  • Disability, disabilities, intellectual, in autosomal recessive mental retardation
  • Disability, disabilities, intellectual, in SATB2-associated syndrome
  • Disability, disabilities, intellectual, in SETBP1 disorder
  • Disability, disabilities, intellectual, in STXBP1 encephalopathy with epilepsy
  • Disability, disabilities, intellectual, in X-linked mental retardation

Parent code

  • F78.AOther genetic related intellectual disabilitiesHeader

Related codes

  • F78.A1SYNGAP1-related intellectual disabilityBillable

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