G71.3

Mitochondrial myopathy, not elsewhere classified

Billable / specific

G71.3 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Excludes1

Not coded here — never report together with this code.

Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.21)
Leigh's encephalopathy (G31.82)
mitochondrial metabolism disorders (E88.4.-)
Reye's syndrome (G93.7)

Not included here — may be reported together when both conditions exist.

certain conditions originating in the perinatal period (P04-P96) (from G71)
certain infectious and parasitic diseases (A00-B99) (from G71)
complications of pregnancy, childbirth and the puerperium (O00-O9A) (from G71)
congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) (from G71)
endocrine, nutritional and metabolic diseases (E00-E88) (from G71)
injury, poisoning and certain other consequences of external causes (S00-T88) (from G71)
neoplasms (C00-D49) (from G71)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from G71)
arthrogryposis multiplex congenita (Q74.3) (from G71)
metabolic disorders (E70-E88) (from G71)
myositis (M60.-) (from G71)