I27.21

Secondary pulmonary arterial hypertension

Billable / specificHCC V28 226

I27.21 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

(Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
(Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension

Not coded here — never report together with this code.

Not included here — may be reported together when both conditions exist.

certain conditions originating in the perinatal period (P04-P96) (from I27)
certain infectious and parasitic diseases (A00-B99) (from I27)
complications of pregnancy, childbirth and the puerperium (O00-O9A) (from I27)
congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) (from I27)
endocrine, nutritional and metabolic diseases (E00-E88) (from I27)
injury, poisoning and certain other consequences of external causes (S00-T88) (from I27)
neoplasms (C00-D49) (from I27)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from I27)
systemic connective tissue disorders (M30-M36) (from I27)
transient cerebral ischemic attacks and related syndromes (G45.-) (from I27)

An additional code may be needed.

associated conditions if applicable, or adverse effects of drugs or toxins, such as:
adverse effect of appetite depressants (T50.5X5)
congenital heart disease (Q20-Q28)
human immunodeficiency virus [HIV] disease (B20)
polymyositis (M33.2-)
portal hypertension (K76.6)
rheumatoid arthritis (M05.-)
schistosomiasis (B65.-)
Sjögren syndrome (M35.0-)
systemic sclerosis (M34.-)
associated underlying condition (from I27.2)

(Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
(Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
Hypertension, hypertensive, pulmonary, arterial
Hypertension, hypertensive, pulmonary, group 1
Hypertension, hypertensive, pulmonary, secondary, arterial