Q03.0

Malformations of aqueduct of Sylvius

Billable / specificHCC V28 182POA exempt

Q03.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Anomaly of aqueduct of Sylvius
  • Obstruction of aqueduct of Sylvius, congenital
  • Stenosis of aqueduct of Sylvius

Includes (from Q03)

  • hydrocephalus in newborn
  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • Arnold-Chiari syndrome, type II (Q07.0-) (from Q03)
  • acquired hydrocephalus (G91.-) (from Q03)
  • hydrocephalus due to congenital toxoplasmosis (P37.1) (from Q03)
  • hydrocephalus with spina bifida (Q05.0-Q05.4) (from Q03)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q03)

Also known as

  • Anomaly of aqueduct of Sylvius
  • Obstruction of aqueduct of Sylvius, congenital
  • Stenosis of aqueduct of Sylvius
  • Anomaly, anomalous, aqueduct of Sylvius
  • Atresia, atretic, aqueduct of Sylvius
  • Hydrocephalus, aqueduct Sylvius stricture
  • Obstruction, obstructed, obstructive, aqueduct of Sylvius, congenital
  • Occlusion, occluded, aqueduct of Sylvius, congenital
  • Septum, septate, aqueduct of Sylvius
  • Stenosis, stenotic, aqueduct of Sylvius
  • Stricture, aqueduct of Sylvius

Parent code

  • Q03Congenital hydrocephalusHeader

Related codes

  • Q03.1Atresia of foramina of Magendie and LuschkaBillable
  • Q03.8Other congenital hydrocephalusBillable
  • Q03.9Congenital hydrocephalus, unspecifiedBillable

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