Q07.01

Arnold-Chiari syndrome with spina bifida

Billable / specificHCC V28 182POA exempt

Q07.01 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from Q07)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • Arnold-Chiari syndrome, type III (Q01.-) (from Q07.0)
  • Arnold-Chiari syndrome, type IV (Q04.8) (from Q07.0)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q07)
  • congenital central alveolar hypoventilation syndrome (G47.35) (from Q07)
  • familial dysautonomia [Riley-Day] (G90.1) (from Q07)
  • neurofibromatosis (nonmalignant) (Q85.0-) (from Q07)

Also known as

  • Arnold-Chiari disease, obstruction or syndrome, with spina bifida
  • Malformation, Chiari, Type II
  • Syndrome, Dandy-Walker, with spina bifida

Parent code

  • Q07.0Arnold-Chiari syndromeHeader

Related codes

  • Q07.00Arnold-Chiari syndrome without spina bifida or hydrocephalusBillable
  • Q07.02Arnold-Chiari syndrome with hydrocephalusBillable
  • Q07.03Arnold-Chiari syndrome with spina bifida and hydrocephalusBillable

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