Q38.0

Congenital malformations of lips, not elsewhere classified

Billable / specificPOA exempt

Q38.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Congenital fistula of lip
  • Congenital malformation of lip NOS
  • Van der Woude's syndrome

Includes (from Q38)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • cleft lip (Q36.-)
  • cleft lip with cleft palate (Q37.-)
  • macrocheilia (Q18.6)
  • microcheilia (Q18.7)
  • dentofacial anomalies (M26.-) (from Q38)
  • macrostomia (Q18.4) (from Q38)
  • microstomia (Q18.5) (from Q38)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q38)

Also known as

  • Congenital fistula of lip
  • Congenital malformation of lip NOS
  • Van der Woude's syndrome
  • Agenesis, lip
  • Anomaly, anomalous, lip
  • Deformity, lipNEC, congenital
  • Ectropion, lip, congenital
  • Fistula, lip, congenital
  • Malformation, lip

Parent code

  • Q38Other congenital malformations of tongue, mouth and pharynxHeader

Related codes

  • Q38.1AnkyloglossiaBillable
  • Q38.2MacroglossiaBillable
  • Q38.3Other congenital malformations of tongueBillable
  • Q38.4Congenital malformations of salivary glands and ductsBillable
  • Q38.5Congenital malformations of palate, not elsewhere classifiedBillable
  • Q38.6Other congenital malformations of mouthBillable
  • Q38.7Congenital pharyngeal pouchBillable
  • Q38.8Other congenital malformations of pharynxBillable

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