Q40.0

Congenital hypertrophic pyloric stenosis

Billable / specificHCC V28 78POA exempt

Q40.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Congenital constriction
  • Congenital hypertrophy
  • Congenital spasm
  • Congenital stenosis
  • Congenital stricture

Includes (from Q40)

  • Note: Codes from this chapter are not for use on maternal records

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q40)

Also known as

  • Congenital constriction
  • Congenital hypertrophy
  • Congenital spasm
  • Congenital stenosis
  • Congenital stricture
  • Achalasia, pylorus
  • Constriction, pylorus, congenital
  • Constriction, pylorus, newborn
  • Hypertrophy, hypertrophic, pylorus, congenital
  • Obstruction, obstructed, obstructive, pylorus, congenital
  • PylorospasmNEC, congenital
  • PylorospasmNEC, newborn
  • Spasm, spastic, spasticity, pylorus NEC, congenital
  • Stenosis, stenotic, pylorus, congenital
  • Stricture, pylorus, congenital

Parent code

  • Q40Other congenital malformations of upper alimentary tractHeader

Related codes

  • Q40.1Congenital hiatus herniaBillable
  • Q40.2Other specified congenital malformations of stomachBillable
  • Q40.3Congenital malformation of stomach, unspecifiedBillable
  • Q40.8Other specified congenital malformations of upper alimentary tractBillable
  • Q40.9Congenital malformation of upper alimentary tract, unspecifiedBillable

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