Q43.1

Hirschsprung's disease

Billable / specificHCC V28 78POA exempt

Q43.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Aganglionosis
  • Congenital (aganglionic) megacolon

Includes (from Q43)

  • Note: Codes from this chapter are not for use on maternal records

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q43)

Also known as

  • Aganglionosis
  • Congenital (aganglionic) megacolon
  • Dilatation, colon, congenital
  • Hirschsprung's disease or megacolon
  • Ileus, neurogenic, Hirschsprung's disease or megacolon
  • Macrocolon
  • Megacolon, congenital, congenitum
  • Megacolon, Hirschsprung's
  • Obstruction, obstructed, obstructive, intestine, neurogenic, Hirschsprung's disease or megacolon

Parent code

  • Q43Other congenital malformations of intestineHeader

Related codes

  • Q43.0Meckel's diverticulum (displaced) (hypertrophic)Billable
  • Q43.2Other congenital functional disorders of colonBillable
  • Q43.3Congenital malformations of intestinal fixationBillable
  • Q43.4Duplication of intestineBillable
  • Q43.5Ectopic anusBillable
  • Q43.6Congenital fistula of rectum and anusBillable
  • Q43.7Persistent cloacaBillable
  • Q43.8Other specified congenital malformations of intestineBillable
  • Q43.9Congenital malformation of intestine, unspecifiedBillable

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