Male pseudohermaphroditism, not elsewhere classified
Billable / specificPOA exempt
Q56.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- 46, XY with streak gonads
- Male pseudohermaphroditism NOS
Includes (from Q56)
- Note: Codes from this chapter are not for use on maternal records
Excludes1
Not coded here — never report together with this code.
- androgen insensitivity syndrome (E34.5-) (from Q56)
- syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99) (from Q56)
- 46,XX true hermaphrodite (Q99.1) (from Q56)
- androgen insensitivity syndrome (E34.5-) (from Q56)
- chimera 46,XX/46,XY true hermaphrodite (Q99.0) (from Q56)
- female pseudohermaphroditism with adrenocortical disorder (E25.-) (from Q56)
- pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99) (from Q56)
- pure gonadal dysgenesis (Q99.1) (from Q56)
Excludes2
Not included here — may be reported together when both conditions exist.
Also known as
- 46, XY with streak gonads
- Male pseudohermaphroditism NOS
- Karyotype, 46,XY, with streak gonads
- Pseudohermaphroditism, male
- Pseudohermaphroditism, male, with cleft scrotum
- Pseudohermaphroditism, male, without gonadal disorder
- Rudimentary, uterus, in male
Parent code
- Q56Indeterminate sex and pseudohermaphroditismHeader