Q81.1

Epidermolysis bullosa letalis

Billable / specificPOA exempt

Q81.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Herlitz' syndrome

Includes (from Q81)

  • Note: Codes from this chapter are not for use on maternal records

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q81)

Also known as

  • Herlitz' syndrome
  • Epidermolysis, bullosa, letalis

Parent code

  • Q81Epidermolysis bullosaHeader

Related codes

  • Q81.0Epidermolysis bullosa simplexBillable
  • Q81.2Epidermolysis bullosa dystrophicaBillable
  • Q81.8Other epidermolysis bullosaBillable
  • Q81.9Epidermolysis bullosa, unspecifiedBillable

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