Q87.89

Other specified congenital malformation syndromes, not elsewhere classified

Billable / specificPOA exempt

Q87.89 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from Q87)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q87)

Use additional code

Add a code to identify the following, if applicable.

  • code(s) to identify all associated manifestations (from Q87)

Also known as

  • Birt-Hogg-Dube syndrome
  • Cantrell's syndrome
  • Cerebro-hepato-renal syndrome
  • Syndrome, basal cell nevus
  • Syndrome, Birt-Hogg-Dube syndrome
  • Syndrome, cardiofaciocutaneous
  • Syndrome, congenital, affecting multiple systems NEC
  • Syndrome, congenital, muscular hypertrophy-cerebral
  • Syndrome, Glass
  • Syndrome, Gorlin's
  • Syndrome, Oliver-McFarlane
  • Syndrome, popliteal, web
  • Syndrome, SATB2-associated
  • Syndrome, Snyder-Robinson
  • Web, webbed, popliteal syndrome

Parent code

  • Q87.8Other specified congenital malformation syndromes, not elsewhere classifiedHeader

Related codes

  • Q87.81Alport syndromeBillable
  • Q87.82Arterial tortuosity syndromeBillable
  • Q87.83Bardet-Biedl syndromeBillable
  • Q87.84Laurence-Moon syndromeBillable
  • Q87.85MED13L syndromeBillable
  • Q87.86Kleefstra syndromeBillable
  • Q87.87Hao-Fountain SyndromeBillable
  • Q87.88CTNNB1 syndromeBillable

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