Q89.3

Situs inversus

Billable / specificPOA exempt

Q89.3 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Dextrocardia with situs inversus
  • Mirror-image atrial arrangement with situs inversus
  • Situs inversus or transversus abdominalis
  • Situs inversus or transversus thoracis
  • Transposition of abdominal viscera
  • Transposition of thoracic viscera

Includes (from Q89)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q89)

Also known as

  • Dextrocardia with situs inversus
  • Mirror-image atrial arrangement with situs inversus
  • Situs inversus or transversus abdominalis
  • Situs inversus or transversus thoracis
  • Transposition of abdominal viscera
  • Transposition of thoracic viscera
  • Dextrocardia, with complete transposition of viscera
  • Dextrocardia, with situs inversus
  • Kartagener's syndrome or triad
  • Levocardia, with situs inversus
  • Sinusitis-bronchiectasis-situs inversus
  • Situs inversus or transversus
  • Syndrome, Kartagener's
  • Syndrome, sinusitis-bronchiectasis-situs inversus
  • Transposition, abdominal viscera
  • Transposition, heart, with complete transposition of viscera
  • Transposition, stomach, with general transposition of viscera
  • Transposition, viscera
  • Triad, Kartagener's

Parent code

  • Q89Other congenital malformations, not elsewhere classifiedHeader

Related codes

  • Q89.0Congenital absence and malformations of spleenHeader
  • Q89.1Congenital malformations of adrenal glandBillable
  • Q89.2Congenital malformations of other endocrine glandsBillable
  • Q89.4Conjoined twinsBillable
  • Q89.7Multiple congenital malformations, not elsewhere classifiedBillable
  • Q89.8Other specified congenital malformationsHeader
  • Q89.9Congenital malformation, unspecifiedBillable

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