Systemic mastocytosis
Billable / specific
D47.02 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Includes (from D47)
- Note: Functional activity
- Note: All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
- Note: Morphology [Histology]
- Note: Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
- Note: Primary malignant neoplasms overlapping site boundaries
- Note: A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
- Note: Malignant neoplasm of ectopic tissue
- Note: Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
- Note: Categories D37-D44, and D48 classify by site neoplasms of uncertain behavior, i.e., histologic confirmation whether the neoplasm is malignant or benign cannot be made.
Excludes1
Not coded here — never report together with this code.
Code also
An additional code may be needed.
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Also known as
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
- Disease, diseased, systemic tissue mast cell
- Mast cell, disease, systemic tissue
- Mastocytosis, indolent systemic
- Mastocytosis, isolated bone marrow
- Mastocytosis, systemic, with an associated hematological non-mast cell lineage disease
Parent code
- D47.0Mast cell neoplasms of uncertain behaviorHeader