Q82.2

Congenital cutaneous mastocytosis

Billable / specificPOA exempt

Q82.2 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa

Includes (from Q82)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • cutaneous mastocytosis NOS (D47.01)
  • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
  • malignant mastocytosis (C96.2-)
  • systemic mastocytosis (D47.02)
  • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
  • acrodermatitis enteropathica (E83.2) (from Q82)
  • congenital erythropoietic porphyria (E80.0) (from Q82)
  • pilonidal cyst or sinus (L05.-) (from Q82)
  • Sturge-Weber (-Dimitri) syndrome (Q85.89) (from Q82)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q82)

Also known as

  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa
  • Mastocytosis, cutaneous, congenital
  • Mastocytosis, cutaneous, of neonatal onset
  • Mastocytosis, cutaneous, of newborn onset
  • Urticaria, pigmentosa, congenital
  • Urticaria, pigmentosa, of neonatal onset
  • Urticaria, pigmentosa, of newborn onset

Parent code

  • Q82Other congenital malformations of skinHeader

Related codes

  • Q82.0Hereditary lymphedemaBillable
  • Q82.1Xeroderma pigmentosumBillable
  • Q82.3Incontinentia pigmentiBillable
  • Q82.4Ectodermal dysplasia (anhidrotic)Billable
  • Q82.5Congenital non-neoplastic nevusBillable
  • Q82.6Congenital sacral dimpleBillable
  • Q82.8Other specified congenital malformations of skinBillable
  • Q82.9Congenital malformation of skin, unspecifiedBillable

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