Q85.89

Other phakomatoses, not elsewhere classified

Billable / specificHCC V28 23POA exempt

Q85.89 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome

Includes (from Q85)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • Meckel-Gruber syndrome (Q61.9) (from Q85.8)
  • ataxia telangiectasia [Louis-Bar] (G11.3) (from Q85)
  • familial dysautonomia [Riley-Day] (G90.1) (from Q85)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q85)

Also known as

  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome
  • Angiomatosis, encephalotrigeminal
  • Dimitri-Sturge-Weber disease
  • Kraft-Weber-Dimitri disease
  • Peutz-Jeghers disease or syndrome
  • Phakomatosis, specified NEC
  • Sturgedisease or syndrome
  • Syndrome, Peutz-Jeghers
  • Syndrome, Sturge-Weber

Parent code

  • Q85.8Other phakomatoses, not elsewhere classifiedHeader

Related codes

  • Q85.81PTEN hamartoma tumor syndromeBillable
  • Q85.82Other Cowden syndromeBillable
  • Q85.83Von Hippel-Lindau syndromeBillable

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