Cerebellar ataxia with defective DNA repair
Billable / specificHCC V28 200
G11.3 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Ataxia telangiectasia [Louis-Bar]
Excludes2
Not included here — may be reported together when both conditions exist.
- Cockayne's syndrome (Q87.19)
- other disorders of purine and pyrimidine metabolism (E79.-)
- xeroderma pigmentosum (Q82.1)
- certain conditions originating in the perinatal period (P04-P96) (from G11)
- certain infectious and parasitic diseases (A00-B99) (from G11)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from G11)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) (from G11)
- endocrine, nutritional and metabolic diseases (E00-E88) (from G11)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from G11)
- neoplasms (C00-D49) (from G11)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from G11)
- cerebral palsy (G80.-) (from G11)
- hereditary and idiopathic neuropathy (G60.-) (from G11)
- metabolic disorders (E70-E88) (from G11)
Also known as
- Ataxia telangiectasia [Louis-Bar]
- Ataxia, ataxy, ataxic, cerebellar, with defective DNA repair
- Ataxia, ataxy, ataxic, telangiectasia
- Ataxia-telangiectasia
- Boder-Sedgwick syndrome
- Louis-Bar syndrome
- Syndrome, ataxia-telangiectasia
- Syndrome, Boder-Sedgewick
- Syndrome, Louis-Barré
- Telangiectasia, telangiectasis, ataxic
Parent code
- G11Hereditary ataxiaHeader
Related codes
- G11.0Congenital nonprogressive ataxiaBillable
- G11.1Early-onset cerebellar ataxiaHeader
- G11.2Late-onset cerebellar ataxiaBillable
- G11.4Hereditary spastic paraplegiaBillable
- G11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontiaBillable
- G11.6Leukodystrophy with vanishing white matter diseaseBillable
- G11.8Other hereditary ataxiasBillable
- G11.9Hereditary ataxia, unspecifiedBillable