Q82.1

Xeroderma pigmentosum

Billable / specificPOA exempt

Q82.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from Q82)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • acrodermatitis enteropathica (E83.2) (from Q82)
  • congenital erythropoietic porphyria (E80.0) (from Q82)
  • pilonidal cyst or sinus (L05.-) (from Q82)
  • Sturge-Weber (-Dimitri) syndrome (Q85.89) (from Q82)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q82)

Also known as

  • Atrophoderma, atrophodermia, pigmentosum
  • Epitheliomatosis pigmented
  • Kaposi's, dermatosis
  • Melanosis, lenticularis progressiva
  • Xeroderma, pigmentosum

Parent code

  • Q82Other congenital malformations of skinHeader

Related codes

  • Q82.0Hereditary lymphedemaBillable
  • Q82.2Congenital cutaneous mastocytosisBillable
  • Q82.3Incontinentia pigmentiBillable
  • Q82.4Ectodermal dysplasia (anhidrotic)Billable
  • Q82.5Congenital non-neoplastic nevusBillable
  • Q82.6Congenital sacral dimpleBillable
  • Q82.8Other specified congenital malformations of skinBillable
  • Q82.9Congenital malformation of skin, unspecifiedBillable

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