D68.1

Hereditary factor XI deficiency

Billable / specificHCC V28 112

D68.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Hemophilia C
  • Plasma thromboplastin antecedent [PTA] deficiency
  • Rosenthal's disease

Excludes1

Not coded here — never report together with this code.

  • abnormal coagulation profile NOS (R79.1) (from D68)

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9) (from D68)
  • certain conditions originating in the perinatal period (P00-P96) (from D68)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D68)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D68)
  • endocrine, nutritional and metabolic diseases (E00-E88) (from D68)
  • human immunodeficiency virus [HIV] disease (B20) (from D68)
  • injury, poisoning and certain other consequences of external causes (S00-T88) (from D68)
  • neoplasms (C00-D49) (from D68)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D68)
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1) (from D68)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3) (from D68)

Also known as

  • Hemophilia C
  • Plasma thromboplastin antecedent [PTA] deficiency
  • Rosenthal's disease
  • Deficiency, deficient, anti-hemophilic, factor, C
  • Deficiency, deficient, factor, XI
  • Deficiency, deficient, plasma thromboplastin, antecedent
  • Deficiency, deficient, PTA
  • Disease, diseased, Rosenthal's
  • Hemophilia, C
  • Rosenthal's disease or syndrome

Parent code

  • D68Other coagulation defectsHeader

Related codes

  • D68.0Von Willebrand diseaseHeader
  • D68.2Hereditary deficiency of other clotting factorsBillable
  • D68.3Hemorrhagic disorder due to circulating anticoagulantsHeader
  • D68.4Acquired coagulation factor deficiencyBillable
  • D68.5Primary thrombophiliaHeader
  • D68.6Other thrombophiliaHeader
  • D68.8Other specified coagulation defectsBillable
  • D68.9Coagulation defect, unspecifiedBillable

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