D68.2

Hereditary deficiency of other clotting factors

Billable / specificHCC V28 112

D68.2 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency

Excludes1

Not coded here — never report together with this code.

  • abnormal coagulation profile NOS (R79.1) (from D68)

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9) (from D68)
  • certain conditions originating in the perinatal period (P00-P96) (from D68)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D68)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D68)
  • endocrine, nutritional and metabolic diseases (E00-E88) (from D68)
  • human immunodeficiency virus [HIV] disease (B20) (from D68)
  • injury, poisoning and certain other consequences of external causes (S00-T88) (from D68)
  • neoplasms (C00-D49) (from D68)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D68)
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1) (from D68)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3) (from D68)

Also known as

  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency
  • Absence, fibrinogen
  • Afibrinogenemia, congenital
  • Defect, defective, coagulation, hereditary NEC
  • Defect, defective, fibrin polymerization
  • Defect, defective, Hageman
  • Deficiency, deficient, accelerator globulin
  • Deficiency, deficient, AC globulin
  • Deficiency, deficient, activating factor
  • Deficiency, deficient, autoprothrombin, I
  • Deficiency, deficient, autoprothrombin, C
  • Deficiency, deficient, clotting factor NEC
  • Deficiency, deficient, coagulation NOS, clotting factor NEC

Parent code

  • D68Other coagulation defectsHeader

Related codes

  • D68.0Von Willebrand diseaseHeader
  • D68.1Hereditary factor XI deficiencyBillable
  • D68.3Hemorrhagic disorder due to circulating anticoagulantsHeader
  • D68.4Acquired coagulation factor deficiencyBillable
  • D68.5Primary thrombophiliaHeader
  • D68.6Other thrombophiliaHeader
  • D68.8Other specified coagulation defectsBillable
  • D68.9Coagulation defect, unspecifiedBillable

Browse