Hereditary hypogammaglobulinemia
Billable / specificHCC V28 115
D80.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Autosomal recessive agammaglobulinemia (Swiss type)
- X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
Includes (from D80)
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes1
Not coded here — never report together with this code.
Excludes2
Not included here — may be reported together when both conditions exist.
- autoimmune disease (systemic) NOS (M35.9) (from D80)
- certain conditions originating in the perinatal period (P00-P96) (from D80)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D80)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D80)
- endocrine, nutritional and metabolic diseases (E00-E88) (from D80)
- human immunodeficiency virus [HIV] disease (B20) (from D80)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from D80)
- neoplasms (C00-D49) (from D80)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D80)
- human immunodeficiency virus [HIV] disease (B20) (from D80)
Also known as
- Autosomal recessive agammaglobulinemia (Swiss type)
- X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
- Absence, gamma globulin in blood, hereditary
- Agammaglobulinemia, autosomal recessive
- Agammaglobulinemia, Bruton's X-linked
- Agammaglobulinemia, congenital sex-linked
- Agammaglobulinemia, hereditary
- Agammaglobulinemia, Swiss type
- Agammaglobulinemia, X-linked
- Bruton's X-linked agammaglobulinemia
- Deficiency, deficient, gammaglobulin in blood, hereditary
- Hypogammaglobulinemia, hereditary
- Immunodeficiency, autosomal recessive, Swiss type
- Syndrome, antibody deficiency, agammaglobulinemic, hereditary
- Syndrome, antibody deficiency, congenital
- Syndrome, antibody deficiency, hypogammaglobulinemic, hereditary
Parent code
- D80Immunodeficiency with predominantly antibody defectsHeader
Related codes
- D80.1Nonfamilial hypogammaglobulinemiaBillable
- D80.2Selective deficiency of immunoglobulin A [IgA]Billable
- D80.3Selective deficiency of immunoglobulin G [IgG] subclassesBillable
- D80.4Selective deficiency of immunoglobulin M [IgM]Billable
- D80.5Immunodeficiency with increased immunoglobulin M [IgM]Billable
- D80.6Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemiaBillable
- D80.7Transient hypogammaglobulinemia of infancyBillable
- D80.8Other immunodeficiencies with predominantly antibody defectsBillable
- D80.9Immunodeficiency with predominantly antibody defects, unspecifiedBillable