D80.1

Nonfamilial hypogammaglobulinemia

Billable / specific

D80.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
  • Common variable agammaglobulinemia [CVAgamma]
  • Hypogammaglobulinemia NOS

Includes (from D80)

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes1

Not coded here — never report together with this code.

  • autoimmune disease (systemic) NOS (M35.9) (from D80)
  • functional disorders of polymorphonuclear neutrophils (D71-) (from D80)

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9) (from D80)
  • certain conditions originating in the perinatal period (P00-P96) (from D80)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D80)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D80)
  • endocrine, nutritional and metabolic diseases (E00-E88) (from D80)
  • human immunodeficiency virus [HIV] disease (B20) (from D80)
  • injury, poisoning and certain other consequences of external causes (S00-T88) (from D80)
  • neoplasms (C00-D49) (from D80)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D80)
  • human immunodeficiency virus [HIV] disease (B20) (from D80)

Also known as

  • Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
  • Common variable agammaglobulinemia [CVAgamma]
  • Hypogammaglobulinemia NOS
  • Absence, gamma globulin in blood
  • Agammaglobulinemia
  • Agammaglobulinemia, with immunoglobulin-bearing B-lymphocytes
  • Agammaglobulinemia, common variable
  • Arthritis, arthritic, in hypogammaglobulinemia
  • Deficiency, deficient, gammaglobulin in blood
  • Disease, diseased, connective tissue, systemic, in hypogammaglobulinemia
  • Hypogammaglobulinemia
  • Hypogammaglobulinemia, nonfamilial
  • Syndrome, antibody deficiency, agammaglobulinemic
  • Syndrome, antibody deficiency, hypogammaglobulinemic

Parent code

  • D80Immunodeficiency with predominantly antibody defectsHeader

Related codes

  • D80.0Hereditary hypogammaglobulinemiaBillable
  • D80.2Selective deficiency of immunoglobulin A [IgA]Billable
  • D80.3Selective deficiency of immunoglobulin G [IgG] subclassesBillable
  • D80.4Selective deficiency of immunoglobulin M [IgM]Billable
  • D80.5Immunodeficiency with increased immunoglobulin M [IgM]Billable
  • D80.6Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemiaBillable
  • D80.7Transient hypogammaglobulinemia of infancyBillable
  • D80.8Other immunodeficiencies with predominantly antibody defectsBillable
  • D80.9Immunodeficiency with predominantly antibody defects, unspecifiedBillable

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