D81

Combined immunodeficiencies

Non-billable header

D81 is a non-billable header code. Use one of the more specific codes below.

Inclusion terms

Includes

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes1

Not coded here — never report together with this code.

  • autoimmune disease (systemic) NOS (M35.9)
  • functional disorders of polymorphonuclear neutrophils (D71-)
  • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9)
  • certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • human immunodeficiency virus [HIV] disease (B20)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • human immunodeficiency virus [HIV] disease (B20)

More specific codes D81

  • D81.0Severe combined immunodeficiency [SCID] with reticular dysgenesisBillable
  • D81.1Severe combined immunodeficiency [SCID] with low T- and B-cell numbersBillable
  • D81.2Severe combined immunodeficiency [SCID] with low or normal B-cell numbersBillable
  • D81.3Adenosine deaminase [ADA] deficiencyHeader
  • D81.4Nezelof's syndromeBillable
  • D81.5Purine nucleoside phosphorylase [PNP] deficiencyBillable
  • D81.6Major histocompatibility complex class I deficiencyBillable
  • D81.7Major histocompatibility complex class II deficiencyBillable
  • D81.8Other combined immunodeficienciesHeader
  • D81.9Combined immunodeficiency, unspecifiedBillable

Related codes

  • D80Immunodeficiency with predominantly antibody defectsHeader
  • D82Immunodeficiency associated with other major defectsHeader
  • D83Common variable immunodeficiencyHeader
  • D84Other immunodeficienciesHeader
  • D86SarcoidosisHeader
  • D89Other disorders involving the immune mechanism, not elsewhere classifiedHeader

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