Immunodeficiency following hereditary defective response to Epstein-Barr virus
Billable / specific
D82.3 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- X-linked lymphoproliferative disease
Includes (from D82)
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes1
Not coded here — never report together with this code.
Excludes2
Not included here — may be reported together when both conditions exist.
- autoimmune disease (systemic) NOS (M35.9) (from D82)
- certain conditions originating in the perinatal period (P00-P96) (from D82)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D82)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D82)
- endocrine, nutritional and metabolic diseases (E00-E88) (from D82)
- human immunodeficiency virus [HIV] disease (B20) (from D82)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from D82)
- neoplasms (C00-D49) (from D82)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D82)
- human immunodeficiency virus [HIV] disease (B20) (from D82)
Also known as
- X-linked lymphoproliferative disease
- Disease, diseased, lymphoproliferative, X-linked
- Immunodeficiency, following hereditary defective response to Epstein-Barr virus
- Lymphoproliferation, X-linked disease
Parent code
- D82Immunodeficiency associated with other major defectsHeader
Related codes
- D82.0Wiskott-Aldrich syndromeBillable
- D82.1Di George's syndromeBillable
- D82.2Immunodeficiency with short-limbed statureBillable
- D82.4Hyperimmunoglobulin E [IgE] syndromeBillable
- D82.8Immunodeficiency associated with other specified major defectsBillable
- D82.9Immunodeficiency associated with major defect, unspecifiedBillable