Other disorders of fructose metabolism
Billable / specific
E74.19 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Fructose-1, 6-diphosphatase deficiency
Includes (from E74)
- Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Excludes1
Not coded here — never report together with this code.
- muscle phosphofructokinase deficiency (E74.09) (from E74.1)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E74)
- androgen insensitivity syndrome (E34.5-) (from E74)
- congenital adrenal hyperplasia (E25.0) (from E74)
- hemolytic anemias attributable to enzyme disorders (D55.-) (from E74)
- Marfan syndrome (Q87.4-) (from E74)
- 5-alpha-reductase deficiency (E29.1) (from E74)
- diabetes mellitus (E08-E13) (from E74)
- hypoglycemia NOS (E16.2) (from E74)
- increased secretion of glucagon (E16.3) (from E74)
- mucopolysaccharidosis (E76.0-E76.3) (from E74)
Excludes2
Not included here — may be reported together when both conditions exist.
Also known as
- Fructose-1, 6-diphosphatase deficiency
- Deficiency, deficient, aldolase
- Deficiency, deficient, fructose 1,6-diphosphatase
- Deficiency, deficient, fructose-1-phosphate aldolase
- Deficiency, deficient, phosphofructokinase
- Disorder, fructose metabolism, fructose-1, 6-diphosphatase deficiency
- Disorder, fructose metabolism, other specified
- Fructose 1,6 diphosphatase deficiency
- Hyperfructosemia
Parent code
- E74.1Disorders of fructose metabolismHeader