E76.0

Mucopolysaccharidosis, type I

Non-billable header

E76.0 is a non-billable header code. Use one of the more specific codes below.

Inclusion terms

Includes (from E76)

  • Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Excludes1

Not coded here — never report together with this code.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E76)
  • androgen insensitivity syndrome (E34.5-) (from E76)
  • congenital adrenal hyperplasia (E25.0) (from E76)
  • hemolytic anemias attributable to enzyme disorders (D55.-) (from E76)
  • Marfan syndrome (Q87.4-) (from E76)
  • 5-alpha-reductase deficiency (E29.1) (from E76)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Ehlers-Danlos syndromes (Q79.6-) (from E76)

Parent code

  • E76Disorders of glycosaminoglycan metabolismHeader

More specific codes E76.0

  • E76.01Hurler's syndromeBillable
  • E76.02Hurler-Scheie syndromeBillable
  • E76.03Scheie's syndromeBillable

Related codes

  • E76.1Mucopolysaccharidosis, type IIBillable
  • E76.2Other mucopolysaccharidosesHeader
  • E76.3Mucopolysaccharidosis, unspecifiedBillable
  • E76.8Other disorders of glucosaminoglycan metabolismBillable
  • E76.9Glucosaminoglycan metabolism disorder, unspecifiedBillable

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