Mucopolysaccharidosis, type II
Billable / specificHCC V28 49
E76.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Hunter's syndrome
Includes (from E76)
- Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Excludes1
Not coded here — never report together with this code.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E76)
- androgen insensitivity syndrome (E34.5-) (from E76)
- congenital adrenal hyperplasia (E25.0) (from E76)
- hemolytic anemias attributable to enzyme disorders (D55.-) (from E76)
- Marfan syndrome (Q87.4-) (from E76)
- 5-alpha-reductase deficiency (E29.1) (from E76)
Excludes2
Not included here — may be reported together when both conditions exist.
Also known as
- Hunter's syndrome
- Degeneration, degenerative, brain, in Hunter's syndrome
- Hunter's, syndrome
- Mucopolysaccharidosis, Hunter's syndrome
- Mucopolysaccharidosis, type, II
Parent code
- E76Disorders of glycosaminoglycan metabolismHeader