Primary pulmonary hypertension
Billable / specificHCC V28 226
I27.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Heritable pulmonary arterial hypertension
- Idiopathic pulmonary arterial hypertension
- Primary group 1 pulmonary hypertension
- Primary pulmonary arterial hypertension
Excludes1
Not coded here — never report together with this code.
Excludes2
Not included here — may be reported together when both conditions exist.
- certain conditions originating in the perinatal period (P04-P96) (from I27)
- certain infectious and parasitic diseases (A00-B99) (from I27)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from I27)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) (from I27)
- endocrine, nutritional and metabolic diseases (E00-E88) (from I27)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from I27)
- neoplasms (C00-D49) (from I27)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from I27)
- systemic connective tissue disorders (M30-M36) (from I27)
- transient cerebral ischemic attacks and related syndromes (G45.-) (from I27)
Also known as
- Heritable pulmonary arterial hypertension
- Idiopathic pulmonary arterial hypertension
- Primary group 1 pulmonary hypertension
- Primary pulmonary arterial hypertension
- Arrillaga-Ayerza syndrome
- Arteriosclerosis, arteriosclerotic, pulmonary
- Ayerza's disease or syndrome
- Cardiopathia nigra
- Disease, diseased, Ayerza's
- Disease, diseased, heart, black
- Disease, diseased, pulmonary, hypertensive, primary
- Hypertension, hypertensive, lesser circulation
- Hypertension, hypertensive, pulmonary, primary
- Sclerosis, sclerotic, pulmonary, artery
- Syndrome, Arrillaga-Ayerza
- Syndrome, Ayerza
- Syndrome, cardiacos negros
- Syndrome, pulmonary, arteriosclerosis
Parent code
- I27Other pulmonary heart diseasesHeader