Rieger anomaly
Billable / specificPOA exempt
Q13.81 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Axenfeld-Rieger syndrome
Includes (from Q13)
- Note: Codes from this chapter are not for use on maternal records
Excludes2
Not included here — may be reported together when both conditions exist.
- inborn errors of metabolism (E70-E88) (from Q13)
- cleft lip and cleft palate (Q35-Q37) (from Q13)
- congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4) (from Q13)
- congenital malformation of larynx (Q31.-) (from Q13)
- congenital malformation of lip NEC (Q38.0) (from Q13)
- congenital malformation of nose (Q30.-) (from Q13)
- congenital malformation of parathyroid gland (Q89.2) (from Q13)
- congenital malformation of thyroid gland (Q89.2) (from Q13)
Use additional code
Add a code to identify the following, if applicable.
- code for associated glaucoma (H42)
Code also
An additional code may be needed.
- any other associated congenital malformations such as cardiac defects
Also known as
- Axenfeld-Rieger syndrome
- Anomaly, anomalous, Rieger
- Glaucoma, in Rieger anomaly
- Rieger anomaly or syndrome
- Syndrome, Axenfeld-Rieger
Parent code
- Q13.8Other congenital malformations of anterior segment of eyeHeader
Related codes
- Q13.89Other congenital malformations of anterior segment of eyeBillable