Q26.4

Anomalous pulmonary venous connection, unspecified

Billable / specificPOA exempt

Q26.4 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from Q26)

  • Note: Codes from this chapter are not for use on maternal records

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q26)

Also known as

  • Anomaly, anomalous, connection, pulmonary venous
  • Anomaly, anomalous, opening, pulmonary veins
  • Anomaly, anomalous, pulmonary, venous connection
  • Atresia, atretic, vein NEC, pulmonary

Parent code

  • Q26Congenital malformations of great veinsHeader

Related codes

  • Q26.0Congenital stenosis of vena cavaBillable
  • Q26.1Persistent left superior vena cavaBillable
  • Q26.2Total anomalous pulmonary venous connectionBillable
  • Q26.3Partial anomalous pulmonary venous connectionBillable
  • Q26.5Anomalous portal venous connectionBillable
  • Q26.6Portal vein-hepatic artery fistulaBillable
  • Q26.8Other congenital malformations of great veinsBillable
  • Q26.9Congenital malformation of great vein, unspecifiedBillable

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