Other congenital malformations of great veins
Billable / specificPOA exempt
Q26.8 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Absence of vena cava (inferior) (superior)
- Azygos continuation of inferior vena cava
- Persistent left posterior cardinal vein
- Scimitar syndrome
Includes (from Q26)
- Note: Codes from this chapter are not for use on maternal records
Excludes2
Not included here — may be reported together when both conditions exist.
Also known as
- Absence of vena cava (inferior) (superior)
- Azygos continuation of inferior vena cava
- Persistent left posterior cardinal vein
- Scimitar syndrome
- Absence, superior vena cava, congenital
- Absence, veincongenital NEC, great
- Absence, vena cava, congenital
- Agenesis, vein, great NEC
- Agenesis, vena cava
- Anomaly, anomalous, vein, great, specified NEC
- Anomaly, anomalous, venous return
- Atresia, atretic, vein NEC, great
- Atresia, atretic, vena cava
- Azygos, continuation inferior vena cava
- Hypoplasia, hypoplastic, vein, great
- Hypoplasia, hypoplastic, vena cava
- Malformation, great, vein, specified type NEC
- Malposition, congenital, vein, great
- Malposition, congenital, vena cava
Parent code
- Q26Congenital malformations of great veinsHeader
Related codes
- Q26.0Congenital stenosis of vena cavaBillable
- Q26.1Persistent left superior vena cavaBillable
- Q26.2Total anomalous pulmonary venous connectionBillable
- Q26.3Partial anomalous pulmonary venous connectionBillable
- Q26.4Anomalous pulmonary venous connection, unspecifiedBillable
- Q26.5Anomalous portal venous connectionBillable
- Q26.6Portal vein-hepatic artery fistulaBillable
- Q26.9Congenital malformation of great vein, unspecifiedBillable