Q26.8

Other congenital malformations of great veins

Billable / specificPOA exempt

Q26.8 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Absence of vena cava (inferior) (superior)
  • Azygos continuation of inferior vena cava
  • Persistent left posterior cardinal vein
  • Scimitar syndrome

Includes (from Q26)

  • Note: Codes from this chapter are not for use on maternal records

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q26)

Also known as

  • Absence of vena cava (inferior) (superior)
  • Azygos continuation of inferior vena cava
  • Persistent left posterior cardinal vein
  • Scimitar syndrome
  • Absence, superior vena cava, congenital
  • Absence, veincongenital NEC, great
  • Absence, vena cava, congenital
  • Agenesis, vein, great NEC
  • Agenesis, vena cava
  • Anomaly, anomalous, vein, great, specified NEC
  • Anomaly, anomalous, venous return
  • Atresia, atretic, vein NEC, great
  • Atresia, atretic, vena cava
  • Azygos, continuation inferior vena cava
  • Hypoplasia, hypoplastic, vein, great
  • Hypoplasia, hypoplastic, vena cava
  • Malformation, great, vein, specified type NEC
  • Malposition, congenital, vein, great
  • Malposition, congenital, vena cava

Parent code

  • Q26Congenital malformations of great veinsHeader

Related codes

  • Q26.0Congenital stenosis of vena cavaBillable
  • Q26.1Persistent left superior vena cavaBillable
  • Q26.2Total anomalous pulmonary venous connectionBillable
  • Q26.3Partial anomalous pulmonary venous connectionBillable
  • Q26.4Anomalous pulmonary venous connection, unspecifiedBillable
  • Q26.5Anomalous portal venous connectionBillable
  • Q26.6Portal vein-hepatic artery fistulaBillable
  • Q26.9Congenital malformation of great vein, unspecifiedBillable

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