Q33.0

Congenital cystic lung

Billable / specificPOA exempt

Q33.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Congenital cystic lung disease
  • Congenital honeycomb lung
  • Congenital polycystic lung disease

Includes (from Q33)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • cystic fibrosis (E84.0)
  • cystic lung disease, acquired or unspecified (J98.4)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q33)

Also known as

  • Congenital cystic lung disease
  • Congenital honeycomb lung
  • Congenital polycystic lung disease
  • Cyst, bronchogenic, congenital
  • Cyst, congenital NEC, lung
  • Cyst, lung, congenital
  • Cystic, lung disease, congenital
  • Disease, diseased, cystic, lung, congenital
  • Disease, diseased, lung, cystic, congenital
  • Disease, diseased, lung, polycystic, congenital
  • Disease, diseased, polycystic, lung or pulmonary, congenital
  • Honeycomb lung, congenital
  • Polycystic, lung, congenital

Parent code

  • Q33Congenital malformations of lungHeader

Related codes

  • Q33.1Accessory lobe of lungBillable
  • Q33.2Sequestration of lungBillable
  • Q33.3Agenesis of lungBillable
  • Q33.4Congenital bronchiectasisBillable
  • Q33.5Ectopic tissue in lungBillable
  • Q33.6Congenital hypoplasia and dysplasia of lungBillable
  • Q33.8Other congenital malformations of lungBillable
  • Q33.9Congenital malformation of lung, unspecifiedBillable

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