Q87.2

Congenital malformation syndromes predominantly involving limbs

Billable / specificPOA exempt

Q87.2 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Holt-Oram syndrome
  • Klippel-Trenaunay-Weber syndrome
  • Nail patella syndrome
  • Rubinstein-Taybi syndrome
  • Sirenomelia syndrome
  • Thrombocytopenia with absent radius [TAR] syndrome
  • VATER syndrome

Includes (from Q87)

  • Note: Codes from this chapter are not for use on maternal records

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q87)

Use additional code

Add a code to identify the following, if applicable.

  • code(s) to identify all associated manifestations (from Q87)

Also known as

  • Holt-Oram syndrome
  • Klippel-Trenaunay-Weber syndrome
  • Nail patella syndrome
  • Rubinstein-Taybi syndrome
  • Sirenomelia syndrome
  • Thrombocytopenia with absent radius [TAR] syndrome
  • VATER syndrome
  • Fong's syndrome
  • Klippel-Trenaunaysyndrome
  • Mietens' syndrome
  • Nail, patella syndrome
  • Onycho-osteodysplasia
  • Osteo-onycho-arthro-dysplasia
  • Osteo-onychodysplasia, hereditary
  • Österreicher-Turner syndrome
  • Sirenomelia
  • Syndrome, Fong's
  • Syndrome, nail patella
  • Syndrome, Osterreicher-Turner
  • Syndrome, sirenomelia

Parent code

  • Q87Other specified congenital malformation syndromes affecting multiple systemsHeader

Related codes

  • Q87.0Congenital malformation syndromes predominantly affecting facial appearanceBillable
  • Q87.1Congenital malformation syndromes predominantly associated with short statureHeader
  • Q87.3Congenital malformation syndromes involving early overgrowthBillable
  • Q87.4Marfan syndromeHeader
  • Q87.5Other congenital malformation syndromes with other skeletal changesBillable
  • Q87.8Other specified congenital malformation syndromes, not elsewhere classifiedHeader
  • Q87.ALoeys-Dietz syndromeBillable

Browse