Q87.A

Loeys-Dietz syndrome

Billable / specificNew in FY2027POA exempt

Q87.A is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from Q87)

  • Note: Codes from this chapter are not for use on maternal records

Excludes1

Not coded here — never report together with this code.

  • arterial tortuosity syndrome (Q87.82)
  • Ehlers-Danlos syndrome (Q79.6)
  • Marfan syndrome (Q87.40-Q87.43)
  • other systemic involvement of connective tissue (M35)

Excludes2

Not included here — may be reported together when both conditions exist.

  • inborn errors of metabolism (E70-E88) (from Q87)

Use additional code

Add a code to identify the following, if applicable.

  • code(s) to identify all associated manifestations (from Q87)

Also known as

  • Syndrome, Loeys-Dietz

Parent code

  • Q87Other specified congenital malformation syndromes affecting multiple systemsHeader

Related codes

  • Q87.0Congenital malformation syndromes predominantly affecting facial appearanceBillable
  • Q87.1Congenital malformation syndromes predominantly associated with short statureHeader
  • Q87.2Congenital malformation syndromes predominantly involving limbsBillable
  • Q87.3Congenital malformation syndromes involving early overgrowthBillable
  • Q87.4Marfan syndromeHeader
  • Q87.5Other congenital malformation syndromes with other skeletal changesBillable
  • Q87.8Other specified congenital malformation syndromes, not elsewhere classifiedHeader

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