Alpha thalassemia
Billable / specific
D56.0 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Alpha thalassemia major
- Hemoglobin H Constant Spring
- Hemoglobin H disease
- Hydrops fetalis due to alpha thalassemia
- Severe alpha thalassemia
- Triple gene defect alpha thalassemia
Excludes1
Not coded here — never report together with this code.
Excludes2
Not included here — may be reported together when both conditions exist.
- autoimmune disease (systemic) NOS (M35.9) (from D56)
- certain conditions originating in the perinatal period (P00-P96) (from D56)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D56)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D56)
- endocrine, nutritional and metabolic diseases (E00-E88) (from D56)
- human immunodeficiency virus [HIV] disease (B20) (from D56)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from D56)
- neoplasms (C00-D49) (from D56)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D56)
Use additional code
Add a code to identify the following, if applicable.
- code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
Also known as
- Alpha thalassemia major
- Hemoglobin H Constant Spring
- Hemoglobin H disease
- Hydrops fetalis due to alpha thalassemia
- Severe alpha thalassemia
- Triple gene defect alpha thalassemia
- Disease, diseased, hemoglobin or Hb, Bart's
- Disease, diseased, hemoglobin or Hb, H
- Disease, diseased, hemoglobin or Hb, H, Constant Spring
- Hb, Bart's disease
- Hemoglobin, H Constant Spring
- Hydrops, fetalis, due to alpha thalassemia
- Hydrops, newborn, due to alpha thalassemia
- Thalassemia, alpha
Parent code
- D56ThalassemiaHeader