E74.00

Glycogen storage disease, unspecified

Billable / specificHCC V28 50

E74.00 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Includes (from E74)

  • Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Excludes1

Not coded here — never report together with this code.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E74)
  • androgen insensitivity syndrome (E34.5-) (from E74)
  • congenital adrenal hyperplasia (E25.0) (from E74)
  • hemolytic anemias attributable to enzyme disorders (D55.-) (from E74)
  • Marfan syndrome (Q87.4-) (from E74)
  • 5-alpha-reductase deficiency (E29.1) (from E74)
  • diabetes mellitus (E08-E13) (from E74)
  • hypoglycemia NOS (E16.2) (from E74)
  • increased secretion of glucagon (E16.3) (from E74)
  • mucopolysaccharidosis (E76.0-E76.3) (from E74)

Excludes2

Not included here — may be reported together when both conditions exist.

  • Ehlers-Danlos syndromes (Q79.6-) (from E74)

Also known as

  • Aglycogenosis
  • Disease, diseased, glycogen storage
  • Disease, diseased, glycogen storage, generalized
  • Disorder, tubulo-interstitial, glycogen storage disease
  • Myopathy, in glycogen storage disease
  • Nephritis, nephritic, tubulo-interstitial, due to glycogen storage disease

Parent code

  • E74.0Glycogen storage diseaseHeader

Related codes

  • E74.01von Gierke diseaseBillable
  • E74.02Pompe diseaseBillable
  • E74.03Cori diseaseBillable
  • E74.04McArdle diseaseBillable
  • E74.05Lysosome-associated membrane protein 2 [LAMP2] deficiencyBillable
  • E74.09Other glycogen storage diseaseBillable

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